A 9-year-old child presented with scoliosis. On examination, there is a bony spur seen overlying the lumbar vertebrae with an overlying tuft of hair along with multiple vertebral anomalies. The most likely diagnosis is (AIPG 2009)
|A||Caudal regression syndrome|
|C||Dorsal dermal sinus|
|D|| Tight filum terminale|
Diastematomyelia - intraspinal anomalies, such as tethering of the conus medullaris below L1, splitting of the spinal cord (diastematomyelia)
a. 50% occurs between L1 and L3, 25% between T7 and Tl2
b. Windened interpedicular distances are common, but not necessarily at the same level as the spur.
c. The spur is visible in 33% of cases and extends from the neural arch forward.
d. Laminar fusion associated with a neural arch defect at the same or adjacent level are important signs in predicting the presence of diastematomyelia ± associated meningocoele, neurenteric cyst or dermoid.