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Dermatology

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Blistering Diseases

Question
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A person with recurrent oral ulcers with yellow base erythematous surrounding & nodules in extensor aspect of legs diagnosis is (AIIMS May 2013)



A Beh|et’s syndrome
B Pemphigus

C Herpes genitalis
D Fixed drug eruption

Ans. A
Beh|et's syndrome

Ref: CMDT (Current Medical Diagnosis & Treatment) 2013, Chapter 20, page 872

1). Beh|et's syndrome is a rare immune-mediated systemic vasculitis that often presents with mucous membrane ulceration and ocular involvements.

2). Beh|et disease (BD) was named in 1937 after the Turkish dermatologist Hulusi Beh|et, who first described the triple-symptom complex of recurrent oral aphthous ulcers, genital ulcers, and uveitis.

3). As a systemic disease, it can also involve visceral organs such as the gastrointestinal tract, pulmonary, musculoskeletal, and neurological systems.

4). This syndrome can be fatal, due to ruptured vascular aneurysms, or severe neurological complications.

5). Nearly all patients present with some form of painful oral mucocutaneous ulcerations in the form of aphthous ulcers or non-scarring oral lesions.

6). The oral lesions are similar to those found in inflammatory bowel disease and can be relapsing.

7). Painful genital ulcerations usually develop around the anus, vulva or scrotum and cause scarring in 75% of the patients.

8). Additionally, patients may present with erythema nodosum, cutaneous pustular vasculitis, and lesions similar to pyoderma gangrenosum.

9). ISG criteria for diagnosis of Behcet’s Syndrome:

a. Major Criteria: Multiple oral ulcers

b. Minor Criteria: 1). Genital Ulcers, 2). Eye involvement, 3). Skin inv., 4). Pathergy Test

c. One major and two minor criteria are required for diagnosis.

Blistering Diseases Flashcard List

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