Features of Potter syndrome are (AIPG 2012)
|A||B/L renal agenesis|
|C||Widely separately eyes|
|D||All of the above|
All of the above
1. Renal agenesis: Potter syndrome: B/L renal agenesis, pulmonary hypoplasia, Potter facies (widely separated eyes, low set ears, receding chin, epicanthic folds, Nose is broad and compressed, limb anomalies). There is history of maternal oligohydramnios.
2. Renal dysplasia, Multicystic kidney:
a. Renal dysplasia is abnormal development of renal parenchyma (primitive structures are present).
b. Multicystic dysplastic kidney is the most common cause of abdominal mass in the newborn. No intervention is usually required.
c. These may got infected or cause HT.
d. VUR is present in 15% of contralateral kidney.