Amino Acids, Proteins and Porphyrins
Which amino acid causes hypoglycemia
Causes of Persistent Neonatal Hypoglycemia (Blood glucose< 4Omg/dL):-
a. Hyper insulin states: -
i. Beta-cell Hyper plasia (NESIDIOBLASTOSIS)
ii. Adenoma of β-cells.
iii. LEUCINE sensitivity
b. Deficiency of substrate such as in
i. Ketotic hypoglycemia and
ii. Maple syrup urine disease — in which blood and urine-levels of LEUCINE ISOLEUCINE and VALINE are elevated.
c. Glycogen storage disease and fructose intolerance.
No, doubt, the best answer is Leucine.